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KMID : 1155520170120040335
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Anesthesia and Pain Medicine
2017 Volume.12 No. 4 p.335 ~ p.338
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Experience with reversal of a neuromuscular block with sugammadex in a child with Prader-Willi syndrome - A case report -
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Sung Tae-Yun
Kang Tae-Yoon
Cho Choon-Kyu
Kwon Hee-Uk
Kang Po-Soon
Jee Young-Seok
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Abstract
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We treated a 4-year-old patient with a genetic disorder, Prader?Willi syndrome, that was accompanied by pulmonary hypertension due to upper airway obstruction. Prader?Willi syndrome is a complex genetic condition characterized by hypotonia, feeding difficulties, poor growth, and delayed development. Hypotonia was the main concern in the anesthetic management of this patient, including the choice of a neuromuscular blocking agent. We report successful induction of anesthesia in this patient with sevoflurane inhalation, remifentanil infusion, and a non-depolarizing muscle relaxant, rocuronium, while following up the status of the neuromuscular block by train-of-four monitoring and reversing the neuromuscular block with sugammadex.
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KEYWORD
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Hypotonia, Prader-Willi syndrome, Pulmonary hypertension, Remifentanil, Rocuronium, Sugammadex.
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